ABSTRACT
Behçet’s disease is a chronic relapsing multisystem disease of unknown etiology. The manifestations of the disease are: recurrent aphthous stomatitis, genital ulcerations, other mucocutaneous lesions, ocular, articular, neurological, urogenital, cardiovascular, gastrointestinal and pulmonary manifestations. Vascular complications are a common component of this disease but cardiac involvement is a very rare and the sign of poor prognosis. A 48-year-old male patient presented with dyspnea, atypical chest pain, and haemoptysis. In his past history; he was unremarkable except for Behçet's disease. Further investigations revealed a free right atrial thrombus and pulmonary thromboembolism. We preferred medical management which consisted of immunosuppressive drugs and anticoagulation. On a follow-up period of three months we observed complete dissolution of the thrombus and dramatic improvement of clinical status.