ABSTRACT

Kommerell diverticulum is a rare phenomenon: Aberrant left subclavian artery in association with right aortic arch and ventricular septal defect.

Kommerell´s diverticulum can occur in a number of anomalies of the aortic arch system that can, but do not always, cause symptoms of tracheal or esophageal compression. The diverticulum is most frequently present in cases of right aortic arch with an aberrant left subclavian artery. In this anomaly, the left subclavian artery arises from the right-sided aortic arch as the 4th branch and extends behind the esophagus to the left arm. The descending aorta can be right sided or left sided. We report a 5-year-old girl with Kommerel diverticulum, minor left upper abnormality and restrictive perimembraneous ventricular septal defect.