ABSTRACT
Haemangiopericytoma is a soft tissue tumor derived from mesenchymal cells with pericytic differentiation. This tumor involves mostly the lower extremity and retro peritoneum and rarely the head and neck region. Surgery has been suggested the gold standard of the treatment with additional benefits if radiotherapy is taken. Here, we report the case of a Haemangiopericytoma in a 32- year old male patient. The tumor was discovered incidentally during the follow up clinical examination of his oro-nasal closure. Wide excision of the tumor was performed, and radiation therapy was administered. At the end of the one-year follow up, no recurrence was detected. Haemagiopericytoma is an uncommon vascular tumor with unpredictable behavior, which necessitates a life-long follow up period. Due to the lack of data about this rare entity, further clinical reports and systematic reviews are essential.