ABSTRACT
Leiomyosarcomas located on the vena cava inferior are extremely rare tumours. Although radical surgical resection of the tumor is the most important factor on survival, greatly advanced tumors are encountered since the disease may present with delayed symptoms. This situation makes the resection with clear border difficult. Chemotheraphy, radiotheraphy or combined treatment regimens may be performed to the patients after surgery. One of the important issues in the treatment of inferior vena cava leiomyosarcomas is how to reconstruct the inferior vena cava. In this case report, the successful surgical treatment of a case who admitted with the complaints of abdominal pain and nausea and diagnosed to have inferior vena cava leiomyosarcoma is presented.