Congenital bilateral perisylvian syndrome: a case report
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Case Report
P: 64-66
March 2009

Congenital bilateral perisylvian syndrome: a case report

Gulhane Med J 2009;51(1):64-66
1. GATF Çocuk Sağlığı ve Hastalıkları Anabilim Dalı
2. GATF Radyodiagnostik Radyoloji Anabilim Dalı
3. GATF Tıbbi Genetik Bilim Dalı
No information available.
No information available
Received Date: 21.09.2007
Accepted Date: 31.03.2008
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ABSTRACT

Congenital bilateral perisylvian syndrome is a rare syndrome characterized with mental retardation, speech retardation, pseudobulbar palsy, epilepsy and bilateral neuronal migration defects in the perisylvian area on brain magnetic rezonans imaging. It may be due to genetic or non-genetic reasons. We herein report a case presenting with complex partial seizures, speech retardation, bilateral fascial diplegia and polymicrogyria findings on brain magnetic resonance imaging and diagnosed to have congenital bilateral perisylvian syndrome as it is very rare.

Keywords: Epilepsy, congenital bilateral perisylvian syndrome, perisylvian cortical dysplasia, pseudobulbar palsy

References

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