Case Report

Congenital bilateral perisylvian syndrome: a case report

  • Sebahattin Vurucu
  • A. Oğuz Afyoncu
  • Murat Kocaoğlu
  • Davut Gül
  • Rıdvan Akın

Received Date: 21.09.2007 Accepted Date: 31.03.2008 Gulhane Med J 2009;51(1):64-66

Congenital bilateral perisylvian syndrome is a rare syndrome characterized with mental retardation, speech retardation, pseudobulbar palsy, epilepsy and bilateral neuronal migration defects in the perisylvian area on brain magnetic rezonans imaging. It may be due to genetic or non-genetic reasons. We herein report a case presenting with complex partial seizures, speech retardation, bilateral fascial diplegia and polymicrogyria findings on brain magnetic resonance imaging and diagnosed to have congenital bilateral perisylvian syndrome as it is very rare.

Keywords: Epilepsy, congenital bilateral perisylvian syndrome, perisylvian cortical dysplasia, pseudobulbar palsy