Pulmonary sequestration is a congenital anomaly of the lobe or segment of the lungs that has no connection with normal tracheobronchial tree and has a vascular supply from systemic arteries. Persistent left superior vena cava is the draning of venous blood of head and neck to the right atrium totally or partially via coronary sinus. We want to report an intralober sequestration case we have operated which has a persistent left superior vena cava at the same time as being a first in the literatüre. Fifty year old woman admitted to our clinic with the complaint of pain in left lateral inferior thoracic field. Tests revealed intralobar sequestration in left lower lobe, persistent left superior vena cava, hypoplasia of left pulmonary artery and volume loss in left lung. No concomittan cardiac defect was found. Surgery was performed to the sequestrated lobe. No complication occured in the postoperative period. The patient was informed about her vascular anomaly of the heart and told to inform the physician performing central catheterisation and cardiac surgery. Association of persistent left superior vena cava and intrapulmonary sequestration is a very rare entity. Patients like our case we present, should be evaluated carefully. Especially bleedings from the aberran arteries can be when dissecting the sequestrated parancyma. We suggest these patients to be operated in experienced clinics.
Keywords: Intralobar sequestration, persistent left superior vena cava, pulmonary artery, vena cava superior .
